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Педиатрическая фармакология

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Современные подходы к ведению детей с атипичным гемолитико-уремическим синдромом

https://doi.org/10.15690/pf.v19i2.2400

Полный текст:

Аннотация

Экспертами Союза педиатров России разработаны актуальные клинические рекомендации по оказанию медицинской помощи детям с атипичным гемолитико-уремическим синдромом (аГУС). аГУС — ультраредкое (орфанное) заболевание прогрессирующего течения, характеризующееся рецидивированием на протяжении всей жизни и представляющее собой потенциально жизнеугрожающее состояние. В статье подробно рассмотрены вопросы этиологии, патогенеза, классификации заболевания. Особое внимание уделено диагностике, дифференциальной диагностике и терапии аГУС, основанным на принципах доказательности.

Об авторах

Х. М. Эмирова
Московский государственный медико-стоматологический университет им. А.И. Евдокимова; Центр гравитационной хирургии крови и гемодиализа ГБУЗ «Детская городская клиническая больница св. Владимира ДЗМ»
Россия

Москва.


Раскрытие интересов:

Нет



Т. Ю. Абасеева
Московский государственный медико-стоматологический университет им. А.И. Евдокимова; Центр гравитационной хирургии крови и гемодиализа ГБУЗ «Детская городская клиническая больница св. Владимира ДЗМ»
Россия

Москва.


Раскрытие интересов:

Нет



А. А. Баранов
НИИ педиатрии и охраны здоровья детей НКЦ №2 РНЦХ им. акад. Б.В. Петровского; Первый Московский государственный медицинский университет им. И.М. Сеченова (Сеченовский Университет)
Россия

Москва.


Раскрытие интересов:

Нет



Н. Д. Вашакмадзе
НИИ педиатрии и охраны здоровья детей НКЦ №2 РНЦХ им. акад. Б.В. Петровского; Российский национальный исследовательский медицинский университет им. Н.И. Пирогова
Россия

Москва.


Раскрытие интересов:

Нет



Е. А. Вишнева
НИИ педиатрии и охраны здоровья детей НКЦ №2 РНЦХ им. акад. Б.В. Петровского; Российский национальный исследовательский медицинский университет им. Н.И. Пирогова
Россия

Москва.


Раскрытие интересов:

Нет



Г. А. Генералова
Центр гравитационной хирургии крови и гемодиализа ГБУЗ «Детская городская клиническая больница св. Владимира ДЗМ»; Российская медицинская академия непрерывного последипломного образования МЗ РФ
Россия

Москва.


Раскрытие интересов:

Нет



Е. Ю. Захарова
Медико-генетический научный центр им. академика Н.П. Бочкова
Россия

Москва.


Раскрытие интересов:

Нет



Т. А. Калюжная
НИИ педиатрии и охраны здоровья детей НКЦ №2 РНЦХ им. акад. Б.В. Петровского; Российский национальный исследовательский медицинский университет им. Н.И. Пирогова
Россия

Москва.


Раскрытие интересов:

Нет



С. И. Куцев
Медико-генетический научный центр им. академика Н.П. Бочкова
Россия

Москва.


Раскрытие интересов:

Нет



Л. С. Намазова-Баранова
НИИ педиатрии и охраны здоровья детей НКЦ №2 РНЦХ им. акад. Б.В. Петровского; Российский национальный исследовательский медицинский университет им. Н.И. Пирогова; Белгородский государственный национальный исследовательский университет
Россия

Намазова-Баранова Лейла Сеймуровна - доктор медицинских наук, профессор, академик РАН, заведующая кафедрой факультетской педиатрии педиатрического факультета РНИМУ им. Н.И. Пирогова Минздрава России; руководитель НИИ педиатрии и охраны здоровья детей НКЦ №2 РНЦХ им. акад. Б.В. Петровского; президент Союза педиатров России.

119333, Москва, ул. Фотиевой, д. 10.

тел.: +7 (499) 400-47-33


Раскрытие интересов:

Нет



Т. П. Макарова
Казанский Государственный Медицинский Университет
Россия

Казань.


Раскрытие интересов:

Нет



Т. В. Маргиева
Первый Московский государственный медицинский университет им. И.М. Сеченова (Сеченовский Университет)
Россия

Москва.


Раскрытие интересов:

Нет



С. А. Мстиславская
Московский государственный медико-стоматологический университет им. А.И. Евдокимова; Центр гравитационной хирургии крови и гемодиализа ГБУЗ «Детская городская клиническая больница св. Владимира ДЗМ»
Россия

Москва.


Раскрытие интересов:

Нет



А. Л. Музуров
Центр гравитационной хирургии крови и гемодиализа ГБУЗ «Детская городская клиническая больница св. Владимира ДЗМ»; Российская медицинская академия непрерывного последипломного образования МЗ РФ
Россия

Москва.


Раскрытие интересов:

Нет



Т. Е. Панкратенко
Центр гравитационной хирургии крови и гемодиализа ГБУЗ «Детская городская клиническая больница св. Владимира ДЗМ»
Россия

Москва.


Раскрытие интересов:

Нет



М. М. Шилова
Российский национальный исследовательский медицинский университет им. Н.И. Пирогова
Россия

Москва.


Раскрытие интересов:

Нет



М. В. Федосеенко
НИИ педиатрии и охраны здоровья детей НКЦ №2 РНЦХ им. акад. Б.В. Петровского; Российский национальный исследовательский медицинский университет им. Н.И. Пирогова
Россия

Москва.


Раскрытие интересов:

Нет



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Для цитирования:


Эмирова Х.М., Абасеева Т.Ю., Баранов А.А., Вашакмадзе Н.Д., Вишнева Е.А., Генералова Г.А., Захарова Е.Ю., Калюжная Т.А., Куцев С.И., Намазова-Баранова Л.С., Макарова Т.П., Маргиева Т.В., Мстиславская С.А., Музуров А.Л., Панкратенко Т.Е., Шилова М.М., Федосеенко М.В. Современные подходы к ведению детей с атипичным гемолитико-уремическим синдромом. Педиатрическая фармакология. 2022;19(2):127-152. https://doi.org/10.15690/pf.v19i2.2400

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Emirova K.M., Abaseeva T.Yu., Baranov A.A., Vashakmadze N.D., Vishneva E.A., Generalova G.A., Zakharova E.Yu., Kaluzhnaya T.A., Kutsev S.I., Namazova-Baranova L.S., Makarova T.P., Margieva T.V., Mstislavskaya S.A., Muzurov A.L., Pankratenko T.E., Shilova M.M., Fedoseenko M.V. Modern Approaches to the Management of Children with Atypical Hemolytic Uremic Syndrome. Pediatric pharmacology. 2022;19(2):127-152. (In Russ.) https://doi.org/10.15690/pf.v19i2.2400

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