WILSON-MIKITY SYNDROME – A RARE INTERSTITIAL PULMONARY DISEASE IN NEONATES
https://doi.org/10.15690/pf.v11i2.958
Abstract
Wilson-Mikity syndrome is an interstitial pulmonary disease of unknown etiology developing in neonatal period and characterized by late oxygen dependence development. The article cites data the possible etiological factors, pathogenesis, pathomorphology, clinical, X-ray and CT presentation of this rare disease. Having analyzed observations of patients with this syndrome (n=61) found in literature from 1960 to 2008, we identified relation of the syndrome’s manifestation to age and degree of prematurity and disease outcomes. We present results of our observations of 6 patients with Wilson-Mikity syndrome, including data of high resolution computed tomography.
About the Authors
D. Yu. Ovsyannikov
Peoples’ Friendship University of Russia, Moscow
Children’s infectious diseases clinical hospital No. 6 of the Department of Healthcare of Moscow
Russian Federation
head of the pediatrics department at the Peoples’ Friendship University of Russia
Russian Federation
head of the pediatrics department at the Peoples’ Friendship University of Russia
M. A. Belyashova
Peoples’ Friendship University of Russia, Moscow
Russian Federation
Russian Federation
A. A. Krushelnitskiy
Peoples’ Friendship University of Russia, Moscow
Russian Federation
Russian Federation
A. A. Avakyan
Children’s Infectious Diseases Clinical Hospital № 6 of the Department of Healthcare of Moscow, Russian Federation
Russian Federation
Russian Federation
N. O. Zaytseva
Children’s Infectious Diseases Clinical Hospital № 6 of the Department of Healthcare of Moscow, Russian Federation
Russian Federation
Russian Federation
E. A. Degtyaryova
Peoples’ Friendship University of Russia, Moscow
Children’s Infectious Diseases Clinical Hospital № 6 of the Department of Healthcare of Moscow, Russian Federation
Russian Federation
Russian Federation
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Review
For citations:
Ovsyannikov D.Yu., Belyashova M.A., Krushelnitskiy A.A., Avakyan A.A., Zaytseva N.O., Degtyaryova E.A. WILSON-MIKITY SYNDROME – A RARE INTERSTITIAL PULMONARY DISEASE IN NEONATES. Pediatric pharmacology. 2014;11(2):55-60. https://doi.org/10.15690/pf.v11i2.958
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