ppharmПедиатрическая фармакологияPediatric pharmacology1727-57762500-3089Издательство «ПедиатрЪ»10.15690/pf.v11i2.958ppharm-120Research ArticleРЕДКИЕ БОЛЕЗНИRARE DISEASESСИНДРОМ ВИЛЬСОНА–МИКИТИ — РЕДКОЕ ИНТЕРСТИЦИАЛЬНОЕ ЗАБОЛЕВАНИЕ ЛЕГКИХ У НОВОРОЖДЕННЫХWILSON-MIKITY SYNDROME – A RARE INTERSTITIAL PULMONARY DISEASE IN NEONATESОвсянниковД. Ю.OvsyannikovD. Yu.

доктор медицинских наук, заведующий кафедрой педиатрии Российского университета дружбы народов

head of the pediatrics department at the Peoples’ Friendship University of Russia

mdovsyannikov@yahoo.comБеляшоваМ. А.BelyashovaM. A.КрушельницкийА. А.KrushelnitskiyA. A.АвакянА. А.AvakyanA. A.ЗайцеваН. О.ZaytsevaN. O.ДегтярёваЕ. А.DegtyaryovaE. A.Российский университет дружбы народов, Москва Детская инфекционная клиническая больница № 6 Департамента здравоохранения г. Москвы,РоссияPeoples’ Friendship University of Russia, Moscow Children’s infectious diseases clinical hospital No. 6 of the Department of Healthcare of MoscowRussian FederationРоссийский университет дружбы народов, МоскваРоссияPeoples’ Friendship University of Russia, MoscowRussian FederationДетская инфекционная клиническая больница № 6 Департамента здравоохранения г. Москвы, Российская ФедерацияРоссияChildren’s Infectious Diseases Clinical Hospital № 6 of the Department of Healthcare of Moscow, Russian FederationRussian FederationРоссийский университет дружбы народов, Москва Детская инфекционная клиническая больница № 6 Департамента здравоохранения г. Москвы, Российская ФедерацияРоссияPeoples’ Friendship University of Russia, Moscow Children’s Infectious Diseases Clinical Hospital № 6 of the Department of Healthcare of Moscow, Russian FederationRussian Federation201404042014112Педиатрическая фармакология5560Copyright © Овсянников Д.Ю., Беляшова М.А., Крушельницкий А.А., Авакян А.А., Зайцева Н.О., Дегтярёва Е.А., 20142014Овсянников Д.Ю., Беляшова М.А., Крушельницкий А.А., Авакян А.А., Зайцева Н.О., Дегтярёва Е.А.Ovsyannikov D.Y., Belyashova M.A., Krushelnitskiy A.A., Avakyan A.A., Zaytseva N.O., Degtyaryova E.A.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.pedpharma.ru/jour/article/view/120

Wilson-Mikity syndrome is an interstitial pulmonary disease of unknown etiology developing in neonatal period and characterized by late oxygen dependence development. The article cites data the possible etiological factors, pathogenesis, pathomorphology, clinical, X-ray and CT presentation of this rare disease. Having analyzed observations of patients with this syndrome (n=61) found in literature from 1960 to 2008, we identified relation of the syndrome’s manifestation to age and degree of prematurity and disease outcomes. We present results of our observations of 6 patients with Wilson-Mikity syndrome, including data of high resolution computed tomography.

 

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The authors declare that there are no conflicts of interest present.