Sex Cord Tumor with Annular Tubules in a Teenage Girl: Case Study
https://doi.org/10.15690/pf.v22i4.2928
Abstract
Background. Sex cord tumor with annular tubules is a rare ovarian pathology. Its incidence is only 6% of all primary ovarian neoplasms. The clinical signs of this disease are diverse and often individual. The major treatment option is surgery.
Case description. Patient M., 12 years old, was admitted to the hospital with complaints on recurrent genital bleeding. Historical information: patient had suspected dermoid cyst of the right ovary according to ultrasound. The patient was readmitted to the hematology and chemotherapy department due to posthemorrhagic iron deficiency anemia. Next ultrasound has revealed solid mass in the structure of right ovary, 67 × 42 × 54 mm, with active blood flow. Preliminary diagnosis of “D39.1 Neoplasm of uncertain or unknown behavior: Ovary” was made upon admission to the hospital. The mass up to 7 cm in size, low-elastic consistency, painless at palpation has been revealed to the right of the uterus via bimanual examination. Thus, the preliminary diagnosis was confirmed. The tumor of the right ovary was sent for histological examination after its surgical removal. The pathologist concluded that the morphological picture corresponds to sex cord tumor with annular tubules. Oncologist has made the final diagnosis according to pathoanatomical examination: “C56 Malignant neoplasm of ovary”. The patient was suggested to perform additional examination and recommendations were given at discharge to clarify the disease stage and determine the indications for antineoplastic therapy.
Conclusion. Regular admissions to gynecologist are crucial for teenage girls since many diseases can have subtle or no clinical signs.
About the Authors
Elena V. Sibirskaya
Pirogov Russian National Research Medical University
Russian Federation
Disclosure of interest:
Russian Federation
MD, PhD, Professor
Moscow
Disclosure of interest:
Not declared.
Irina V. Karachentsova
Pirogov Russian National Research Medical University
Russian Federation
Disclosure of interest:
Russian Federation
MD, PhD
1, Ostrovityanova Str., building 7, Moscow, 117997, +7 (925) 505-31-04
Disclosure of interest:
Not declared.
Mariya S. Dolzhnikova
Pirogov Russian National Research Medical University
Russian Federation
Disclosure of interest:
Russian Federation
student
Moscow
Disclosure of interest:
Not declared.
Polina O. Nikiforova
Pirogov Russian National Research Medical University
Russian Federation
Disclosure of interest:
Russian Federation
MD
Moscow
Disclosure of interest:
Not declared.
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Review
For citations:
Sibirskaya E.V., Karachentsova I., Dolzhnikova M.S., Nikiforova P.O. Sex Cord Tumor with Annular Tubules in a Teenage Girl: Case Study. Pediatric pharmacology. 2025;22(4):386-390. (In Russ.) https://doi.org/10.15690/pf.v22i4.2928
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