COMPREHENSIVE APPROACH TO SEVERITY ASSESSMENT OF CARDIOVASCULAR HEMODYNAMIC DISORDERS IN PATIENTS WITH RHABDOMYOMAS
https://doi.org/10.15690/pf.v14i3.1745
Abstract
Space-occupying lesions in the heart refer to a rare congenital pathology with incidence of 0.32% in pediatric practice. In recent years, the detection frequency of this pathology has increased due to the achievements of early diagnostics (including prenatal diagnostics), integration of high volume scanning and high-quality ultrasound images. The greatest number of tumors (72–77%) is detected in infants under 1 year of age, up to 26% of which — prenatally. Available international clinical data confirms the congenital nature of most heart tumors, approximately 50% are rhabdomyomas. The presented clinical case demonstrates the demand for a complex approach and the application of new 3D and 4D cardiac scanning in pediatric practice to assess the severity of cardiovascular damage and the prognosis of treatment in patients with rhabdomyomas of the heart.
About the Authors
Gregory V. RevunenkovRussian Federation
Moscow
Tatyana N. Petrenets
Russian Federation
Moscow
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Review
For citations:
Revunenkov G.V., Petrenets T.N. COMPREHENSIVE APPROACH TO SEVERITY ASSESSMENT OF CARDIOVASCULAR HEMODYNAMIC DISORDERS IN PATIENTS WITH RHABDOMYOMAS. Pediatric pharmacology. 2017;14(3):198-201. (In Russ.) https://doi.org/10.15690/pf.v14i3.1745