Modern Approaches to the Diagnosis and Management of Children With Primary Ciliary Dyskinesia
A. A. Baranov,
L. S. Namazova-Baranova,
E. A. Vishneva,
L. R. Selimzyanova,
O. I. Simonova,
E. V. Sereda,
N. N. Rozinova,
E. N. Tzygina,
L. K. Katosova,
A. V. Lazareva,
Yu. V. Gorinova,
O. V. Kustova https://doi.org/10.15690/pf.v14i1.1700
Abstract
The article presents the most modern positions of healthcare delivery for children with primary ciliary dyskinesia. Symptoms of this pathology in clinical practice vary that is conditioned by genetic heterogeneity of the disease. The most common disease manifestation in children is frequent inflammatory diseases of the upper and lower respiratory tract. They are recorded in most patients, especially in young children, and the diagnosis is often determined untimely due to a low awareness of specialists about this nosology. Differential diagnostic approach is described in detail, peculiarities of treatment and management of children with this nosology are specified. The material is based on clinical guidelines developed and approved by the professional association «Union of Pediatricians of Russia».
About the Authors
A. A. Baranov
National Scientific and Practical Center of Children’s Health of the Ministry of Health of the Russian Federation
Russian Federation
Russian Federation
L. S. Namazova-Baranova
National Scientific and Practical Center of Children’s Health of the Ministry of Health of the Russian Federation
Pirogov Russian National Research Medical University
Russian Federation
Russian Federation
E. A. Vishneva
National Scientific and Practical Center of Children’s Health of the Ministry of Health of the Russian Federation
Russian Federation
Russian Federation
L. R. Selimzyanova
National Scientific and Practical Center of Children’s Health of the Ministry of Health of the Russian Federation
I.M. Sechenov First Moscow State Medical University
Russian Federation
Russian Federation
O. I. Simonova
National Scientific and Practical Center of Children’s Health of the Ministry of Health of the Russian Federation
I.M. Sechenov First Moscow State Medical University
Russian Federation
Russian Federation
E. V. Sereda
National Scientific and Practical Center of Children’s Health of the Ministry of Health of the Russian Federation
Russian Federation
Russian Federation
N. N. Rozinova
Pirogov Russian National Research Medical University
Russian Federation
Russian Federation
E. N. Tzygina
National Scientific and Practical Center of Children’s Health of the Ministry of Health of the Russian Federation
Russian Federation
Russian Federation
L. K. Katosova
National Scientific and Practical Center of Children’s Health of the Ministry of Health of the Russian Federation
Russian Federation
Russian Federation
A. V. Lazareva
National Scientific and Practical Center of Children’s Health of the Ministry of Health of the Russian Federation
Russian Federation
Russian Federation
Yu. V. Gorinova
National Scientific and Practical Center of Children’s Health of the Ministry of Health of the Russian Federation
Russian Federation
Russian Federation
O. V. Kustova
National Scientific and Practical Center of Children’s Health of the Ministry of Health of the Russian Federation
Russian Federation
Russian Federation
References
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3. Shapiro AJ, Zariwala MA, Ferkol T, et al. Diagnosis, monitoring, and treatment of primary ciliary dyskinesia: PCD foundation consensus recommendations based on state of the art review. Pediatr Pulmonol. 2015;51(2):115–132. doi: 10.1002/ppul.23304.
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Review
For citations:
Baranov A.A., Namazova-Baranova L.S., Vishneva E.A., Selimzyanova L.R., Simonova O.I., Sereda E.V., Rozinova N.N., Tzygina E.N., Katosova L.K., Lazareva A.V., Gorinova Yu.V., Kustova O.V. Modern Approaches to the Diagnosis and Management of Children With Primary Ciliary Dyskinesia. Pediatric pharmacology. 2017;14(1):43-48. (In Russ.) https://doi.org/10.15690/pf.v14i1.1700
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