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TUBULAR DISORDERS WITH RICKETS-LIKE SYNDROME

Abstract

Often under the guise of «ordinary» Rickets are more severe kidney diseases, developing as a result of inherited or acquired, primary or secondary defects in the renal tubules. Incorrect diagnosis leads to an inadequate therapy, rapid progression of disease and renal failure. The article describes the main approaches to the diagnosis and treatment of disorders of tubular rachitis similar syndrome, presents a number of clinical cases in author's practice.
Key words: tubulopathy, acidosis, electrolyte disorders, rickets, rickets-like syndrome, diagnostics, treatment, children.

About the Authors

N.N. Kartamysheva
Scientific Center of Children’s Health, Russian Academy of Medical Sciences, Moscow
Russian Federation


T.V. Vashurina
Scientific Center of Children’s Health, Russian Academy of Medical Sciences, Moscow
Russian Federation



A.M. Mazo
Scientific Center of Children’s Health, Russian Academy of Medical Sciences, Moscow
Russian Federation


A.B. Sugak
Scientific Center of Children’s Health, Russian Academy of Medical Sciences, Moscow
Russian Federation


E.N. Tsygina
Scientific Center of Children’s Health, Russian Academy of Medical Sciences, Moscow
Russian Federation


M.I. Bakanov
Scientific Center of Children’s Health, Russian Academy of Medical Sciences, Moscow
Russian Federation




A.N. Tsygin
Scientific Center of Children’s Health, Russian Academy of Medical Sciences, Moscow
Russian Federation


Review

For citations:


Kartamysheva N., Vashurina T., Mazo A., Sugak A., Tsygina E., Bakanov M., Tsygin A. TUBULAR DISORDERS WITH RICKETS-LIKE SYNDROME. Pediatric pharmacology. 2011;8(4):140-145.

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ISSN 1727-5776 (Print)
ISSN 2500-3089 (Online)