Hypoplastic Left Heart Syndrome: Diagnostic Difficulties in Prenatal Period
https://doi.org/10.15690/pf.v18i5.2331
Abstract
The article discusses the possible diagnostic errors in the hypoplastic left heart syndrome (HLHS) with mitral atresia and intact interventricular septum. “Atrioventricular canal defects” can be commonly and mistakenly diagnosed the prenatal period in such cases. The aspects and possibilities of differential diagnosis of these defects in the prenatal period are discussed. Ultrasound sign is presented in the article, we have named it “hockey stick with puck” that characterizes the retrograde blood flow in the aortic arch. This sign is diagnosed by color Doppler mapping of the sagittal section of the ductus arteriosus and can serve as a marker of mitral/aortic atresia.
About the Authors
Nodira M. Normuradova
Center for the Development of Professional Qualifications of Medical Workers
Uzbekistan
Disclosure of interest:
Uzbekistan
Nodira M. Normuradova
Ts 44-37, Chilanzar, 79097, Tashkent
Disclosure of interest:
Not declared
Аkram A. Fazilov
Center for the Development of Professional Qualifications of Medical Workers
Uzbekistan
Disclosure of interest:
Uzbekistan
Аkram A. Fazilov
Ts 44-37, Chilanzar, 79097, Tashkent
Disclosure of interest:
Not declared
Munisa M. Rasulova
Center for the Development of Professional Qualifications of Medical Workers
Uzbekistan
Disclosure of interest:
Uzbekistan
Munisa M. Rasulova
Ts 44-37, Chilanzar, 79097, Tashkent
Disclosure of interest:
Not declared
References
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Review
For citations:
Normuradova N.M., Fazilov А.A., Rasulova M.M. Hypoplastic Left Heart Syndrome: Diagnostic Difficulties in Prenatal Period. Pediatric pharmacology. 2021;18(5):416-422. (In Russ.) https://doi.org/10.15690/pf.v18i5.2331
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