ppharmПедиатрическая фармакологияPediatric pharmacology1727-57762500-3089Издательство «ПедиатрЪ»10.15690/pf.v22i1.2850ppharm-2577Research ArticleКЛИНИЧЕСКИЙ СЛУЧАЙCASE REPORTКлинический случай аномальных маточных кровотечений и наружного генитального эндометриоза у пациентки 14 лет с идиопатической тромбоцитопенической пурпуройAbnormal Uterine Bleeding and External Genital Endometriosis in a 14-Year-Old Patient with Idiopathic Thrombocytopenic Purpura: Case Reporthttps://orcid.org/0000-0002-4540-6341СибирскаяЕ. В.SibirskayaElena V.

Сибирская Елена Викторовна, д.м.н., профессор

Москва 

MD, PhD, Professor

Moscow

elsibirskaya@yandex.ruhttps://orcid.org/0000-0002-0254-690XКараченцоваИ. В.KarachentsovaIrina V.

Караченцова Ирина Васильевна, к.м.н. 

Москва 

MD, PhD

Moscow

5053104@list.ruhttps://orcid.org/0000-0002-2348-1607КурмангалееваА. Ю.KurmangaleevaAliya Yu.

Курмангалеева Алия Юнусовна, врач акушер-гинеколог

119049, Москва, 4-й Добрынинский пер., д. 1/9

тел.: +7 (985) 445-14-06 

MD 

1/9, 4th Dobryninsky pereulok, Moscow 119049 

 

askarova-aliya@yandex.ruhttps://orcid.org/0009-0006-0400-0974АннакулиеваА. С.AnnakulievaAina S.

Аннакулиева Айна Сердаровна

Москва 

MD 

Moscow

i-nuxa@mail.ruРНИМУ им. Н.И. Пирогова (Пироговский Университет); РДКБ РНИМУ им. Н.И. Пирогова (Пироговский Университет); Морозовская ДГКБ; Российский университет медициныРоссияPirogov Russian National Research Medical University; Russian Children’s Clinical Hospital of Pirogov Russian National Research Medical University; Morozov Children’s City Clinical Hospital; The Russian University of MedicineRussian FederationРНИМУ им. Н.И. Пирогова (Пироговский Университет); РДКБ РНИМУ им. Н.И. Пирогова (Пироговский Университет)РоссияPirogov Russian National Research Medical University; Russian Children’s Clinical Hospital of Pirogov Russian National Research Medical UniversityRussian FederationРНИМУ им. Н.И. Пирогова (Пироговский Университет); Морозовская ДГКБРоссияPirogov Russian National Research Medical University; Morozov Children’s City Clinical HospitalRussian FederationРДКБ РНИМУ им. Н.И. Пирогова (Пироговский Университет)РоссияRussian Children’s Clinical Hospital of Pirogov Russian National Research Medical UniversityRussian Federation20252602202522142–48Copyright © Сибирская Е.В., Караченцова И.В., Курмангалеева А.Ю., Аннакулиева А.С., 20252025Сибирская Е.В., Караченцова И.В., Курмангалеева А.Ю., Аннакулиева А.С.Sibirskaya E.V., Karachentsova I.V., Kurmangaleeva A.Y., Annakulieva A.S.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.pedpharma.ru/jour/article/view/2577

Обоснование. Идиопатическая тромбоцитопеническая пурпура является одним из наиболее распространенных приобретенных нарушений свертываемости крови у подростков. Данное заболевание характеризуется повышенным риском развития сопутствующих гинекологических патологий, таких как аномальные маточные кровотечения, опухоли и опухолевидные образования яичников, наружный генитальный эндометриоз, что требует тщательного медицинского наблюдения и при необходимости оперативного вмешательства. Описание клинического случая. Рассматривается клинический случай 14-летней пациентки с идиопатической тромбоцитопенической пурпурой, осложненной наружным генитальным эндометриозом и аномальными маточными кровотечениями. Пациентке выполнено оперативное вмешательство в объеме «лапароскопическая оофорэктомия», что позволило предотвратить развитие тяжелых осложнений. Заключение. Данный случай подчеркивает важность комплексного и междисциплинарного подхода к лечению пациенток с идиопатической тромбоцитопенической пурпурой и сопутствующими гинекологическими патологиями, что способствует минимизации риска развития жизнеугрожающих осложнений

Background. Idiopathic Thrombocytopenic Purpura is one of the most common acquired blood-clotting disorders in adolescents. This disease is characterized by an increased risk of developing concomitant gynecological pathologies, such as abnormal uterine bleeding, ovarian tumors and tumor-like masses, external genital endometriosis, which requires careful medical supervision and, if necessary, surgical intervention. Case report. A clinical event of a 14-year-old patient with idiopathic thrombocytopenic purpura complicated by external genital endometriosis and abnormal uterine bleeding is being considered. The patient underwent surgery in the amount of laparoscopic oophorectomy, which prevented the development of severe complications. Conclusion. This case gives accent to the importance of a comprehensive and interdisciplinary approach to the treatment of patients with idiopathic thrombocytopenic purpura and concomitant gynecological pathologies, which helps minimize the risk of life-threatening complications.

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The authors declare that there are no conflicts of interest present.