ppharmПедиатрическая фармакологияPediatric pharmacology1727-57762500-3089Издательство «ПедиатрЪ»10.15690/pf.v21i6.2811ppharm-2549Research ArticleКЛИНИЧЕСКИЙ СЛУЧАЙCASE REPORTКожная форма мастоцитоза: клинический случайCutaneous mastocytosis: Clinical Casehttps://orcid.org/0000-0003-4732-4515ИбишеваА. Х.IbishevaAset Kh.

Ибишева Асет Хамидовна, врач-педиатр, аллерголог-иммунолог 

364028, Грозный, ул. Бисултанова, д. 101

Aset Kh. Ibisheva, MD

101, Bisultanova Str., Grozny, 364028

ibisheva18@mail.ruШахгирееваМ. Р.ShakhgireevaMadina R.

Шахгиреева Мадина Руслановна

Грозный

Madina R. Shakhgireeva, MD

Grozny

zlata-28@mail.ruДжабраиловаЛ В.-М.DzhabrailovaLinda V.-M.

Джабраилова Линда Ваха-Мурадовна

Грозный

Linda V.-M. Dzhabrailova, MD

Grozny

djabrailova.linda@mail.ruХильдихароеваА. Б.KhildikharoevaAsya B.

Хильдихароева Ася Багаудиновна

Грозный

Asya B. Khildikharoeva, MD

Grozny

asya.khildikharoeva@mai.ruУспановаЛ. С.UspanovaLinda S.

Успанова Линда Сулиймановна

Грозный

[Linda S. Uspanova, MD

Grozny

linda.uspanova96@mail.ruГетаеваК. А.-Р.GetaevaKamilaA. A.-R.

Гетаева Камила Абдул-Рахитовна

Грозный

Kamila A.-R. Getaeva, MD

Grozny

kamila.getaeva.93@mai.ruРеспубликанская детская клиническая больница им. Е.П. ГлинкиРоссияRepublican Children’s Clinical Hospital named after E.P. GlinkaRussian Federation202409012025216492495Copyright © Ибишева А.Х., Шахгиреева М.Р., Джабраилова Л.В., Хильдихароева А.Б., Успанова Л.С., Гетаева К.А., 20242024Ибишева А.Х., Шахгиреева М.Р., Джабраилова Л.В., Хильдихароева А.Б., Успанова Л.С., Гетаева К.А.Ibisheva A.K., Shakhgireeva M.R., Dzhabrailova L.V., Khildikharoeva A.B., Uspanova L.S., GetaevaKamila A.A.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.pedpharma.ru/jour/article/view/2549

В практике врача аллерголога-иммунолога часто встречается кожный синдром, требующий дифференциальной диагностики. Одним из редких кожных заболеваний у детей является мастоцитоз, который обусловлен избыточным накоплением тучных клеток в различных органах. Наиболее распространенной формой у детей является кожный мастоцитоз. Дебют заболевания возможен в любом возрасте. Патогномоничным признаком мастоцитоза считается положительный симптом Дарье. Представленный клинический случай демонстрирует классическую картину кожной формы мастоцитоза.

Skin syndrome is common in the practice of allergologist-immunologist, and it requires differential diagnosis. One of the rare skin diseases among children is mastocytosis caused by excessive accumulation of mast cells in various organs. Cutaneous Mastocytosis is the most common form in children. The disease onset may occur at any age. The pathognomonic symptom of mastocytosis is positive Darier sign. The presented clinical case demonstrates typical picture of cutaneous mastocytosis.

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The authors declare that there are no conflicts of interest present.