ppharmПедиатрическая фармакологияPediatric pharmacology1727-57762500-3089Издательство «ПедиатрЪ»10.15690/pf.v14i1.1701ppharm-1501Research ArticleВ ПРАКТИКУ ПЕДИАТРАFor Pediatricians' PracticeБаллонная дилатация стриктур пищевода у детей с буллезным эпидермолизом: описание серии случаевBalloon Dilatation of Esophageal Strictures in Children With Bullous Epidermolysis: Description of Case Serieshttps://orcid.org/0000-0003-4299-3269ТупыленкоА. В.TupylenkoA. V.

аспирант ФГАУ «ННПЦЗД» Минздрава России по специальности «детская хирургия» Адрес: 119991, Москва, Ломоносовский пр-т, д. 2, стр. 1, тел.: +7 (499) 134-04-12

tupylenkoav@mail.ruhttps://orcid.org/0000-0002-8305-7592ЛохматовМ. М.LohmatovM. M.https://orcid.org/0000-0003-2252-8570МурашкинН. Н.MurashkinN. N.https://orcid.org/0000-0002-8563-6002ДьяконоваЕ. Ю.DyakonovaE. Y.https://orcid.org/0000-0003-2948-9228ФилиновИ. В.FilinovI. V.https://orcid.org/0000-0003-2820-3099МаксимоваС. А.MaksimovaS. A.https://orcid.org/0000-0002-4107-4642ЕпишевР. В.EpishevR. V.https://orcid.org/0000-0002-5483-0128СурковаИ. А.SurkovaI. A.https://orcid.org/0000-0002-7379-7298БудкинаТ. Н.BudkinaT. N.https://orcid.org/0000-0002-8805-8164ОлдаковскийВ. И.OldakovskyV. I.Национальный научно-практический центр здоровья детейРоссияNational Scientific and Practical Center of Children’s Health of the Ministry of Health of the Russian FederationRussian Federation2017030520171414954Copyright © Тупыленко А.В., Лохматов М.М., Мурашкин Н.Н., Дьяконова Е.Ю., Филинов И.В., Максимова С.А., Епишев Р.В., Суркова И.А., Будкина Т.Н., Олдаковский В.И., 20172017Тупыленко А.В., Лохматов М.М., Мурашкин Н.Н., Дьяконова Е.Ю., Филинов И.В., Максимова С.А., Епишев Р.В., Суркова И.А., Будкина Т.Н., Олдаковский В.И.Tupylenko A.V., Lohmatov M.M., Murashkin N.N., Dyakonova E.Y., Filinov I.V., Maksimova S.A., Epishev R.V., Surkova I.A., Budkina T.N., Oldakovsky V.I.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.pedpharma.ru/jour/article/view/1501

Стриктуры пищевода — наиболее часто встречающиеся осложнения буллезного эпидермолиза у детей. Стриктуры являются причиной развития дисфагии, препятствующей пероральному питанию и поступлению адекватного количества питательных веществ, что сопровождается нарушением нутритивного статуса, потерей веса и задержкой физического развития ребенка. Нарушенный акт глотания также может стать причиной аспирационного синдрома, пневмонии и обструкции дыхательных путей. Для устранения дисфагии и снижения риска возникновения осложнений требуется восстановление проходимости пищевода. В статье представлено описание результатов рентгенассистированной баллонной дилатации у 19 детей с буллезным эпидермолизом и дисфагией. Показано, что этот метод реканализации пищевода позволяет эффективно и безопасно возобновить пероральное кормление детей уже в первые сутки после вмешательства с постепенным расширением рациона питания.

Esophageal strictures are the most common complications of bullous epidermolysis in children. Strictures cause the development of dysphagia that prevents oral alimentation and receipt of an adequate amount of nutrients that is accompanied by a violation of nutritional status, weight loss, and delayed physical development of a child. Disturbed swallowing can also cause aspiration syndrome, pneumonia, and airway obstruction. To eliminate dysphagia and reduce the risk of complications, it is necessary to restore esophageal patency. The article describes the results of X-ray with assisted balloon dilatation in 19 children with bullous epidermolysis and dysphagia. It is shown that this method of esophagus recanalization allows to effectively and safely restore oral alimentation of children already in the first day after intervention with a gradual expansion of the diet.

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The authors declare that there are no conflicts of interest present.